软骨外胚层发育不良相关蛋白抗体,Anti-EVC1抗体

抗体（antibody）指机体的免疫系统在抗原刺激下，由B淋巴细胞或记忆细胞增殖分化成的浆细胞所产生的、可与相应抗原发生特异性结合的免疫球蛋白。主要分布在血清中，也分布于组织液及外分泌液中。
软骨外胚层发育不良相关蛋白抗体,Anti-EVC1抗体  产品信息：
中文名称：软骨外胚层发育不良相关蛋白抗体   
英文名称：Anti-EVC1
产品编号：byk-11282R
产品规格：0.1ml/0.2ml  
产品用途：科研实验
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软骨外胚层发育不良相关蛋白抗体,Anti-EVC1抗体  介绍：
EVC is an autosomal skeletal dysplasia caused by mutations in the EVC and EVC2 genes. Found in developing ribs, heart, kidney and lung, the EVC gene is responsible for normal development of the face, limbs, teeth and nails. The protein expressed by the EVC gene is an intracellular component of the hedgehog signal pathway that contains a leucine zipper and transmembrane domain. Defects in the EVC gene can lead to short-limb dwarfism, ectodermal dysplasia and cardiac anomalies such as irregular atrioventricular septum development. Additionally, the EVC gene has been implicated in Weyers acrodental dysostosis, an autosomal dominant disease characterized by facial abnormalities and limb defects  
保存条件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
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Anti-Defensin β1(mouse rat)  防御素β1抗体(小鼠、大鼠)
Anti-Defensin β1(human)  防御素β1抗体(人)
Anti-DEK oncogene (DNA binding)  DEK癌基因结合蛋白
Anti-Defensin β2/beta-defensin 2/BD-2（to mouse）  防御素β2抗体（小鼠）
Anti-Defensin β2/beta-defensin 2/BD-2（to rat）  防御素β2抗体（大鼠）
Anti-DAP-5/p97 (Death Associated Protein-5)  死亡相关蛋白5抗体
Anti-DAPK1（Death associated protein kinase 1）  凋亡相关蛋白激酶1抗体
Anti-DAPK2（Death associated protein kinase 2）  凋亡相关蛋白激酶2抗体
Anti-DAPK3（Death associated protein kinase 3）  凋亡相关蛋白激酶3抗体
Anti-Deltex-1  DTX1 (Deltex protein 1)