抗体描述: 产品名称:Rabbit anti-Collagen III Polyclonal Antibody 产品别名:Alpha 1 type III collagen; Alpha1 (III) collagen; CO3A1_HUMAN; COL 3A1; COL3A1; Collagen alpha 1(III) chain; Collagen alpha-1(III) chain; Collagen III alpha 1 chain precursor; Collagen III alpha 1 polypeptide; Collagen type III alpha 1 (Ehlers Danlos synd 特异性:Collagen III Antibody detects endogenous levels of total Collagen III. 来源:Rabbit 反应种属:Human,Mouse,Rat 克隆性:Polyclonal 保存方法:Store at -20 °C for one year. Avoid repeated freeze/thaw cycles 产品描述:Defects in COL3A1 are a cause of Ehlers-Danlos syndrome type 3 (EDS3) [MIM:130020]; also known as benign hypermobility syndrome. EDS is a connective tissue disorder characterized by hyperextensible skin, atrophic cutaneous scars due to tissue fragility and joint hyperlaxity. EDS3 is a form of Ehlers-Danlos syndrome characterized by marked joint hyperextensibility without skeletal deformity. 用途范围: WB 1:1000, IHC 1:50-1:200, IF 1:100-1:500, ELISA(peptide) 1:20000-1:40000 产品信息订购: 产品货号 | 产品名称 | 规格 | 价格 | 大包装及货期 | abs131560 | Rabbit anti-Collagen III Polyclonal Antibody | 50ug | 950 | 立即咨询 | 产品更多信息请进入爱必信网站咨询 |