品名 | anti- Alpha galactosidase A antibody |
货号 | FNab00328 |
规格 | 100µg |
状态 | liquid |
纯化方法 | Immunogen affinity purified |
纯度 | ≥95% as determined by SDS-PAGE |
宿主 | Rabbit |
亚型 | IgG |
存储 | PBS with 0.02% sodium azide and 50% glycerol pH 7.3,-20℃ for 24 months(Avoid repeated freeze / thaw cycles.) |
背景介绍 | GLA, also named as Melibiase, Agalsidas and Alpha-galactosidase A, Belongs to the glycosyl hydrolase 27 family. It hydrolysis of terminal, non-reducing alpha-D-galactose residues in alpha-D-galactosides, including galactose oligosaccharides, galactomannans and galactolipids. Fabry disease is an X-linked lysosomal storage disorder resulting from the deficient activity of GLA. Enzyme replacement therapy(ERT) with GLA is currently the most effective therapeutic strategy for patients with Fabry disease, a lysosomal storage disease. |
免疫原 | galactosidase, alpha |
别称 | Alpha galactosidase A, galactosidase, alpha |
分子量 | 49 kDa |
Uniprot ID | P06280 |
适用种属 | Human, Mouse, Rat |
验证应用 | ELISA, IHC, IP, WB |
建议稀释比例 | WB: 1:500-1:5000; IHC: 1:20-1:200; IP: 1:500-1:5000 |
图片 | | Immunohistochemistry of paraffin-embedded human liver cancer tissue slide using FNab00328(GLA antibody) at dilution of 1:50 |
| HeLa cells were subjected to SDS PAGE followed by western blot with FNab00328(GLA antibody) at dilution of 1:1000 |
注意事项 | Alpha galactosidase A antibody|Alpha galactosidase A抗体仅供科研使用 |
产品链接 | https://www.fn-test.cn/product/FNab00328/ |