产品名称: | Troponin I FS Antibody |
说明书: | 【点击查看详细说明及参考图片】 |
货号: | 252200 |
规格: | 0.1 mg |
产品描述: | Troponin I, fast skeletal muscle (troponin I FS) is the inhibitory subunit of troponin, the thin filament regulatory complex which confers calcium-sensitivity to striated muscle actomyosin ATPase activity. Defects in troponin I FS are a cause of distal arthrogryposis type 2B (DA2B), also known as arthrogryposis multiplex congenita, distal, type 2B (AMCD2B). DA2B is a form of inherited multiple congenital contractures. Affected individuals have vertical talus, ulnar deviation in the hands, severe camptodactyly, and a distinctive face characterized by a triangular shape, prominent nasolabial folds, small mouth and a prominent chin. |
克隆类型: | Rabbit Polyclonal Antibody |
亚型: | Rabbit Ig |
免疫原: | KLH-conjugated synthetic peptide encompassing a sequence within the C-term region of human troponin I FS. |
适用物种: | H, M, R |
应用范围: | E, WB, IHC |
应用说明: | E: 1:10,000-1:50,000; WB: 1:200-1:1,000; IHC: 1:50-1:200 |
别名: | Troponin I, fast skeletal muscle; Troponin I, fast-twitch isoform; TNNI2; DA2B; FSSV; AMCD2B |
形态: | Each vial contains 0.1 mg IgG in 0.1 ml (1 mg/ml) of PBS pH7.4, 2% BSA with 0.09% sodium azide. Antibody was purified by immunogen affinity chromatography. |
保存条件: | Store at -20°C. Minimize freeze-thaw cycles. Product is guaranteed one year from the date of shipment. |
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