【产品介绍】Frataxin is a mitochondrial protein that belongs to the FRATAXIN family. It functions in regulating mitochondrial iron transport and respiration (1). Frataxin is crucial for iron–sulfur cluster (ISC) biosynthesis and plays a primary role in their protein maturation in human cells (2). A reduced level of functional protein results in Friedreich ataxia (1, 2). Frataxin (FXN),Rabbit Monoclonal Antibod Recommended Applications WB Applications and Recommended Dilution Factors WB: 1:1,000 - 10,000 Species Reactivity * Human Frataxin (FXN),Rabbit Monoclonal Antibod *Species cross-reactivity is based on WB analysis. Products Data Western blot analysis on (A) human heart, (B) fetal skin, and (C) PBL lysates using anti-Frataxin RabMAb (cat. #5190-1). Frataxin (FXN),Rabbit Monoclonal Antibod Specificity A synthetic peptide corresponding to residues in human Frataxin was used as an immunogen. |