卵巢滤泡激素抗体(BHD综合征)Anti-FLCN/BHD/Folliculin的产品说明:
--产品介绍:This gene is located within the Smith-Magenis syndrome region on chromosome 17. Mutations in this gene are associated with Birt-Hogg-Dube syndrome, which is characterized by fibrofolliculomas, renal tumors, lung cysts, and pneumothorax. Alternative splicing of this gene results in three transcript variants encoding different isoforms.BHD综合征(Birt-Hogg-Dube综合征)是指:患者患有多发性纤维毛囊瘤,并伴发软垂疣、胶原瘤、脂肪瘤和(或)口腔纤维瘤。是一种显性遗传综合征,有报告BHD患者可伴发髓样癌、结肠癌和肾细胞癌。BHD综合征,主要为纤维毛囊瘤约2~4mm大小,皮肤色丘疹,可单个存在,但常见为多发性,散在分布于颜面、躯干和四肢。另外可伴发软垂疣、胶原瘤、脂肪瘤和(或)口腔纤维瘤。
--该抗体来源于:(Rabbit)
--卵巢滤泡激素抗体(BHD综合征)的参数介绍:
1、浓度:1mg/1ml
2、交叉反应:hu, mo, rat
3、产品类型:一抗
4、研究领域:肿瘤细胞生物免疫学
5、蛋白分子量:predicted molecular weight: 64kDa
6、性状:Lyophilized or Liquid
7、免疫原:KLH conjugated synthetic peptide derived from human FLCN/BHD
8、亚型:polyclonal
9、纯化方法:affinity purified by Protein A
10、储存液:0.01M PBS, pH 7.4 with 10 mg/ml BSA and 0.1% Sodium azide
11、产品应用:WB=1:100-500ELISA=1:500-1000IP=1:20-100IHC-P=1:100-500IHC-F=1:100-500IF=1:100-500 (石蜡切片需做抗原修复) not yet tested in other applications. optimal dilutions/concentrations should be determined by the end user.
12、保存条件:Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
(1mg/1ml卵巢滤泡激素抗体(BHD综合征)Anti-FLCN/BHD/Folliculin,的相关产品:免疫组化常用试剂免疫印迹常用试剂各种标记二抗)